Pediatrics & Neonatology
Volume 49, Issue 2 , Pages 39-42 , April 2008

Macrophage Activation Syndrome as Initial Presentation of Systemic Lupus Erythematosus

Received 27 November 2007 ,Revised 15 January 2008 ,Accepted 25 March 2008.

References 

  1. Kogawa K , Lee SM , Villanueva J , Marmer D , Sumegi J , Filipovich AH . Perforin expression in cytotoxic lymphocytes from patients with hemophagocytic lymphohistiocytosis and their family members . Blood . 2002;99:61–66
  2. Janka G . Familial and acquired hemophagocytic lymphohistiocytosis . Eur J Pediatr . 2007;166:95–109
  3. Ravelli A . Macrophage activation syndrome . Curr Opin Rheumatol . 2002;14:548–552
  4. Henter J-I , Elinder G , Ost A . Diagnostic guidelines for hemophagocytic lymphohistiocytosis. The FHL Study Group of the Histiocyte Society . Semin Oncol . 1991;18:29–33
  5. Janka GE , Schenider EM . Modern management of children with haemophagocytic lymphohistiocytosis . Br J Haematol . 2004;124:4–14
  6. Henter J-I , Tondini C , Pritchard J . Histiocytic syndromes . Crit Rev Oncol Hematol . 2004;50:157–174
  7. Kelly A , Ramanan AV . Recognition and management of macrophage activation syndrome in juvenile arthritis . Curr Opin Rheumotol . 2007;19:477–481
  8. Henter JI , Horne A , Arico M , et al.   HLH–2004: diagnostic and therapeutic guidelines for hemophagocytic lymphohistiocytosis . Pediatr Blood Cancer . 2007;48:124–131
  9. Hadchouel M , Prieur AM , Griscelli C . Acute hemorrhagic, hepatic, and neurologic manifestations in juvenile rheumatoid arthritis: possible relationship to drugs or infection . J Pediatr . 1985;106:561–566
  10. Grom AA . Macrophage activation syndrome and reactive hemophagocytic lymphohistiocytosis: the same entities? . Curr Opin Rheumatol . 2003;15:587–590
  11. Avcin T , Tse SM , Schneider R , Ngan B , Silverman ED . Macrophage activation syndrome as the presenting manifestation of rheumatic diseases in childhood . J Pediatr . 2006;148:683–686
  12. McCann LJ , Hasson N , Pilkington CA . Macrophage activation syndrome as an early presentation of lupus . J Rheumatol . 2006;33:438–440
  13. Benarroch LMK , Sterba G , Bosque M . Macrophage activation syndrome as a debut of systemic lupus erythematosus . J Allergy Clin Immunol . 2006;117:S210
  14. Stephan JL , Kone-Paut I , Galambrun C , Mouy R , BaderMeunier B , Prieur AM . Reactive haemophagocytic syndrome in children with inflammatory disorders: a retrospective study of 24 patients . Rheumatology . 2001;40:1285–1292
  15. Hochberg MC . Updating the American College of Rheumatology revised criteria for the classification of systemic lupus erythematosus . Arthritis Rheum . 1997;40:1725
  16. Tan EM , Cohen AS , Fries JF , et al.   The 1982 revised criteria for the classification of systemic lupus erythematosus . Arthritis Rheum . 1982;25:1271
  17. Smeenk R , Brinkman K , Van den Brink H , et al.   Antibodies to DNA in patients with systemic lupus erythematosus: their role in the diagnosis, the follow-up and the pathogenesis of the disease . Clin Rheumatol . 1990;9(1 Suppl 1):100–110
  18. Chen HH , Kuo HC , Wang L , et al.   Childhood macrophage activation syndrome differs from infection-associated hemophagocytosis syndrome in etiology and outcome in Taiwan . J Microbiol Immunol Infect . 2007;40:265–271
  19. Mouy R , Stephan JL , Pillet P , Haddad E , Hubert P , Prieur AM . Efficacy of cyclosporine A in the treatment of macrophage activation syndrome in juvenile arthritis: report of five cases . J Pediatr . 1996;129:750–754

PII: S1875-9572(08)60010-8

doi: 10.1016/S1875-9572(08)60010-8

Pediatrics & Neonatology
Volume 49, Issue 2 , Pages 39-42 , April 2008

Article Tools