Pediatrics & Neonatology
Volume 49, Issue 2 , Pages 48-51, April 2008

Restrictive Cardiomyopathy in a Child

  • Shan-Miao Lin

      Affiliations

    • Department of Pediatrics, Mackay Memorial Hospital, Taipei, Taiwan
    • ,
  • Haw-Kwei Hwang

      Affiliations

    • Department of Pediatrics, Mackay Memorial Hospital, Taipei, Taiwan
    • ,
  • Ming-Ren Chen

      Affiliations

    • Department of Pediatrics, Mackay Memorial Hospital, Taipei, Taiwan
    • Mackay Medicine, Nursing and Management College, Taipei, Taiwan
    • Corresponding Author InformationCorresponding author. Department of Pediatrics, Mackay Memorial Hospital, No. 92, Section 2, Chung-Shan North Road, Taipei 104, Taiwan

Received 11 January 2008; received in revised form 14 February 2008; accepted 25 March 2008.

Restrictive cardiomyopathy in young children is rare and carries a poor prognosis. We report an 18-month-old girl with poor feeding and abdominal distension. Except for hepatomegaly, no other gastrointestinal abnormalities were found. She had normalsized ventricles but biatrial enlargement. Echocardiography demonstrated normal systolic but impaired diastolic function. Cardiac catheterization revealed a characteristic dip-and-plateau configuration of the right ventricular pressure tracing. The diagnosis turned out to be typical restrictive cardiomyopathy. The patient was maintained on aspirin while awaiting cardiac transplant.

KEY WORDS:  cardiac catheterization , child , restrictive cardiomyopathy

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PII: S1875-9572(08)60012-1

doi:10.1016/S1875-9572(08)60012-1

Pediatrics & Neonatology
Volume 49, Issue 2 , Pages 48-51, April 2008

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