Pediatrics & Neonatology
Volume 51, Issue 1 , Pages 57-60, February 2010

Successful Weaning of a Laryngeal Mask Airway After a Tongue-lip Adhesion Operation in a Case With Cerebro-costo-mandibular Syndrome

  • Chi-Yung So

      Affiliations

    • Division of Genetics, Department of Pediatrics, Chung Shan Medical University Hospital, Taichung, Taiwan
  • ,
  • Yan-Yan Ng

      Affiliations

    • Division of Genetics, Department of Pediatrics, Chung Shan Medical University Hospital, Taichung, Taiwan
  • ,
  • Chih-Yu Peng

      Affiliations

    • Department of Oral and Maxillofacial Surgery, Chung Shan Medical University, Taichung, Taiwan
  • ,
  • Jui-Ming Hu

      Affiliations

    • Division of Genetics, Department of Pediatrics, Chung Shan Medical University Hospital, Taichung, Taiwan
  • ,
  • Suh-Jen Chen

      Affiliations

    • Division of Genetics, Department of Pediatrics, Chung Shan Medical University Hospital, Taichung, Taiwan
  • ,
  • Jia-Yuh Chen

      Affiliations

    • School of Medicine, Chung Shan Medical University, Taichung, Taiwan
  • ,
  • Pen-Hua Su

      Affiliations

    • Division of Genetics, Department of Pediatrics, Chung Shan Medical University Hospital, Taichung, Taiwan
    • School of Medicine, Chung Shan Medical University, Taichung, Taiwan
    • Corresponding Author InformationCorresponding author. Division of Genetics, Department of Pediatrics, Chung Shan Medical University Hospital, 110 Chien-Kuo North Road, Section 1, Taichung, Taiwan

Received 29 December 2008; received in revised form 23 March 2009; accepted 24 April 2009.

Cerebro-costo-mandibular syndrome (CCMS) consists of severe micrognathia, glossoptosis, posterior rib-gap defects and developmental delay. It may cause upper airway obstruction and flail chest, resulting in neonatal hypoxia, and possibly death. Early airway management or surgical intervention to maintain a patent airway is critical to avoid hypoxia in CCMS patients. We report a newborn with CCMS who was successfully weaned from a laryngeal mask after undergoing a tongue–lip adhesion operation at 164 days of age.

Key Words:  airway obstruction , cerebro-costo-mandibular syndrome , tongue-lip adhesion

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PII: S1875-9572(10)60011-3

doi:10.1016/S1875-9572(10)60011-3

Pediatrics & Neonatology
Volume 51, Issue 1 , Pages 57-60, February 2010