Successful Weaning of a Laryngeal Mask Airway After a Tongue-lip Adhesion Operation in a Case With Cerebro-costo-mandibular Syndrome
Received 29 December 2008; received in revised form 23 March 2009; accepted 24 April 2009.
Cerebro-costo-mandibular syndrome (CCMS) consists of severe micrognathia, glossoptosis, posterior rib-gap defects and developmental delay. It may cause upper airway obstruction and flail chest, resulting in neonatal hypoxia, and possibly death. Early airway management or surgical intervention to maintain a patent airway is critical to avoid hypoxia in CCMS patients. We report a newborn with CCMS who was successfully weaned from a laryngeal mask after undergoing a tongue–lip adhesion operation at 164 days of age.
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aDivision of Genetics, Department of Pediatrics, Chung Shan Medical University Hospital, Taichung, Taiwan
bDepartment of Oral and Maxillofacial Surgery, Chung Shan Medical University, Taichung, Taiwan
cSchool of Medicine, Chung Shan Medical University, Taichung, Taiwan
Corresponding author. Division of Genetics, Department of Pediatrics, Chung Shan Medical University Hospital, 110 Chien-Kuo North Road, Section 1, Taichung, Taiwan
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